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Research Pediatrics
University Medical Center Groningen

EC 2.4.1.11

GS1,2

1=Muscle type Glycogen Synt(het)ase (UDPglucose:glycogen 4-A-D-glucosyl transferase

2=liver-type  

Benodigd materiaal: Lever of Fibroblasten

Referenties:

  • Wulf d H, Hers HG, Eur. J. Biochem. 1967 2: 50-56
  • Stalmans W, Wulf d H, Hue L, Hers HG, Eur J. Biochem. 1974, 41:127-134
  • Yuan-Tsong C., Glycogen Storage Diseases.  In:Scriver CR, Beaudet AL, Sly WS, Valle D, eds.The Metabolic and Molecular Bases of Inherited Disease. 2001; 8 edtion: 1521-1553
Last modified:23 February 2015 4.47 p.m.