Echocardiographic features of an atypical presentation of rapidly progressive cardiac amyloidosisBrugts, J. J., Houtgraaf, J., Hazenberg, B. P. C. & Kofflard, M. J., 26-May-2013, In : World Journal of Cardiology. 5, 5, p. 154-156 3 p.
Research output: Contribution to journal › Article › Academic › peer-review
We present the case of a 66 year old male who presented with dyspnea and reduced exercise tolerance. Echocardiography demonstrated impaired left ventricular (LV) function and restrictive diastolic function with pronounced concentric left ventricular hypertrophy (LVH) without a history of hypertension and no aortic valve stenosis. Differential diagnostics of concentric LVH are discussed in detail. In the current case, cardiac amyloidosis (AL) amyloidosis was diagnosed and confirmed by serum amyloid P (SAP) scintigraphy and abdominal fat aspiration biopsy. This case shows the rapid decline in clinical condition with progression of cardiac involvement of AL. As discussed in detail, cardiac involvement in AL-amyloidosis generally denotes a poor prognosis, regardless of the method of treatment.
|Number of pages||3|
|Journal||World Journal of Cardiology|
|Publication status||Published - 26-May-2013|