Publication

18 jaar ervaring met chronische beademing bij patiënten met spierdystrofie van Duchenne

Meinesz, A. F., Bladder, G., Goorhuis, J. F., Fock, J. M., Staal-Schreinemachers, A. L., Zijlstra, J. & Wijkstra, P. J., 18-Aug-2007, In : Nederlands Tijdschrift voor Geneeskunde. 151, 33, p. 1830-1833 4 p.

Research output: Contribution to journalArticleAcademicpeer-review

APA

Meinesz, A. F., Bladder, G., Goorhuis, J. F., Fock, J. M., Staal-Schreinemachers, A. L., Zijlstra, J., & Wijkstra, P. J. (2007). 18 jaar ervaring met chronische beademing bij patiënten met spierdystrofie van Duchenne. Nederlands Tijdschrift voor Geneeskunde, 151(33), 1830-1833.

Author

Meinesz, A F ; Bladder, G ; Goorhuis, J F ; Fock, J M ; Staal-Schreinemachers, A L ; Zijlstra, Jan ; Wijkstra, P J. / 18 jaar ervaring met chronische beademing bij patiënten met spierdystrofie van Duchenne. In: Nederlands Tijdschrift voor Geneeskunde. 2007 ; Vol. 151, No. 33. pp. 1830-1833.

Harvard

Meinesz, AF, Bladder, G, Goorhuis, JF, Fock, JM, Staal-Schreinemachers, AL, Zijlstra, J & Wijkstra, PJ 2007, '18 jaar ervaring met chronische beademing bij patiënten met spierdystrofie van Duchenne' Nederlands Tijdschrift voor Geneeskunde, vol. 151, no. 33, pp. 1830-1833.

Standard

18 jaar ervaring met chronische beademing bij patiënten met spierdystrofie van Duchenne. / Meinesz, A F; Bladder, G; Goorhuis, J F; Fock, J M; Staal-Schreinemachers, A L; Zijlstra, Jan; Wijkstra, P J.

In: Nederlands Tijdschrift voor Geneeskunde, Vol. 151, No. 33, 18.08.2007, p. 1830-1833.

Research output: Contribution to journalArticleAcademicpeer-review

Vancouver

Meinesz AF, Bladder G, Goorhuis JF, Fock JM, Staal-Schreinemachers AL, Zijlstra J et al. 18 jaar ervaring met chronische beademing bij patiënten met spierdystrofie van Duchenne. Nederlands Tijdschrift voor Geneeskunde. 2007 Aug 18;151(33):1830-1833.


BibTeX

@article{456af13ed61f4a7aa368fc29e68b34c8,
title = "18 jaar ervaring met chronische beademing bij pati{\"e}nten met spierdystrofie van Duchenne",
abstract = "OBJECTIVE: To find out which patients with Duchenne muscular dystrophy are eligible for starting home mechanical ventilation and what the survival rate is.DESIGN: Retrospective.METHOD: In 48 patients with Duchenne muscular dystrophy who were treated with home ventilation from 1987, the results were assessed in the follow-up visit in February 2005. Initially, ventilation was only given through a tracheotomy (TPPV), but after starting up a multidisciplinary neuromuscular consultation, non-invasive ventilation (NIPPV) was offered in an earlier stage of the disease. The following data were derived from the outpatient medical record: indication for ventilation, vital capacity (VC), arterial blood gas values, duration of ventilation up to February 2005, survival and causes of death.RESULTS: 15 patients died. The 5-year survival rate was 75{\%} from the start of mechanical ventilation and 67{\%} (18/27) of the patients were still living at home at the time of the follow-up visit. The most important causes of death were cardiomyopathy (5/15) and tracheal bleeding (3/15). The group of patients who started ventilation before 1995 (n = 17) had a significantly smaller VC than the group (n = 31) who started after the neuromuscular consultation was set up. The PaCO2 during daytime was significantly higher in the group that started ventilation before 1995 compared to the group that started later.CONCLUSION: Home mechanical ventilation can be implemented effectively in patients with Duchenne dystrophy, with a 5-year survival of 75{\%}.",
keywords = "Adolescent, Adult, Cause of Death, Child, Female, Home Care Services, Humans, Intermittent Positive-Pressure Ventilation, Male, Muscular Dystrophy, Duchenne, Neuromuscular Diseases, Respiration, Artificial, Respiratory Insufficiency, Retrospective Studies, Survival Analysis, Vital Capacity",
author = "Meinesz, {A F} and G Bladder and Goorhuis, {J F} and Fock, {J M} and Staal-Schreinemachers, {A L} and Jan Zijlstra and Wijkstra, {P J}",
year = "2007",
month = "8",
day = "18",
language = "Dutch",
volume = "151",
pages = "1830--1833",
journal = "Ned Tijdschr Geneeskd",
issn = "0028-2162",
publisher = "NLM (Medline)",
number = "33",

}

RIS

TY - JOUR

T1 - 18 jaar ervaring met chronische beademing bij patiënten met spierdystrofie van Duchenne

AU - Meinesz, A F

AU - Bladder, G

AU - Goorhuis, J F

AU - Fock, J M

AU - Staal-Schreinemachers, A L

AU - Zijlstra, Jan

AU - Wijkstra, P J

PY - 2007/8/18

Y1 - 2007/8/18

N2 - OBJECTIVE: To find out which patients with Duchenne muscular dystrophy are eligible for starting home mechanical ventilation and what the survival rate is.DESIGN: Retrospective.METHOD: In 48 patients with Duchenne muscular dystrophy who were treated with home ventilation from 1987, the results were assessed in the follow-up visit in February 2005. Initially, ventilation was only given through a tracheotomy (TPPV), but after starting up a multidisciplinary neuromuscular consultation, non-invasive ventilation (NIPPV) was offered in an earlier stage of the disease. The following data were derived from the outpatient medical record: indication for ventilation, vital capacity (VC), arterial blood gas values, duration of ventilation up to February 2005, survival and causes of death.RESULTS: 15 patients died. The 5-year survival rate was 75% from the start of mechanical ventilation and 67% (18/27) of the patients were still living at home at the time of the follow-up visit. The most important causes of death were cardiomyopathy (5/15) and tracheal bleeding (3/15). The group of patients who started ventilation before 1995 (n = 17) had a significantly smaller VC than the group (n = 31) who started after the neuromuscular consultation was set up. The PaCO2 during daytime was significantly higher in the group that started ventilation before 1995 compared to the group that started later.CONCLUSION: Home mechanical ventilation can be implemented effectively in patients with Duchenne dystrophy, with a 5-year survival of 75%.

AB - OBJECTIVE: To find out which patients with Duchenne muscular dystrophy are eligible for starting home mechanical ventilation and what the survival rate is.DESIGN: Retrospective.METHOD: In 48 patients with Duchenne muscular dystrophy who were treated with home ventilation from 1987, the results were assessed in the follow-up visit in February 2005. Initially, ventilation was only given through a tracheotomy (TPPV), but after starting up a multidisciplinary neuromuscular consultation, non-invasive ventilation (NIPPV) was offered in an earlier stage of the disease. The following data were derived from the outpatient medical record: indication for ventilation, vital capacity (VC), arterial blood gas values, duration of ventilation up to February 2005, survival and causes of death.RESULTS: 15 patients died. The 5-year survival rate was 75% from the start of mechanical ventilation and 67% (18/27) of the patients were still living at home at the time of the follow-up visit. The most important causes of death were cardiomyopathy (5/15) and tracheal bleeding (3/15). The group of patients who started ventilation before 1995 (n = 17) had a significantly smaller VC than the group (n = 31) who started after the neuromuscular consultation was set up. The PaCO2 during daytime was significantly higher in the group that started ventilation before 1995 compared to the group that started later.CONCLUSION: Home mechanical ventilation can be implemented effectively in patients with Duchenne dystrophy, with a 5-year survival of 75%.

KW - Adolescent

KW - Adult

KW - Cause of Death

KW - Child

KW - Female

KW - Home Care Services

KW - Humans

KW - Intermittent Positive-Pressure Ventilation

KW - Male

KW - Muscular Dystrophy, Duchenne

KW - Neuromuscular Diseases

KW - Respiration, Artificial

KW - Respiratory Insufficiency

KW - Retrospective Studies

KW - Survival Analysis

KW - Vital Capacity

M3 - Article

VL - 151

SP - 1830

EP - 1833

JO - Ned Tijdschr Geneeskd

JF - Ned Tijdschr Geneeskd

SN - 0028-2162

IS - 33

ER -

ID: 23221687